Abstract: [Abstract]Objective:To perform occlusal restoration for dentinogenesis imperfeca with fixed-removable dentures, observe the clinic effect and summarize the clinical experience. Methods: The data of one family of dentinogenesis imperfeca were collected, analysing genetic characteristics of the disease. By making provisional restorations for 3 months. When the occlusion were in a stable condition, the final fixed-removable dentures were made. Patient was followed up 5 years. To evaluate the dentures from safety, strength and suitability, using improved evaluation criteria for the United States Department of public health. Using statistical analysis of non parametric test(a=0.05) for multiple independent samples H Kruskal-Wallis to analyse the data. Results: Family of three successive generations of dentinogenesis imprfecta appeared. The prevalence of offspring was 50%, it is the features of autosomal dominant characteristic. The others were restored using complete dentures. The patient was restored using fixed-removable dentures and followed up 5 years. The patient felt comfortable, the esthetics and mastication function were significantly improved. The clinical examinations show natural color, fitted margin, healthy gums, and no fracture or fall off of the dentures. There were no significant differences in all the evaluation items(P>0.05). Conclusion: Occlusal restoration with fixed-removable dentures may yield favorable clinical effect.

Key words: [Keyword] dentinogenesis imperfeca, fixed-removable denture, Occlusal restoration